A young boy was referred because of recurrent syncope.
He had been investigated one year ago because of syncope at school. At
echocardiography a large mass was detected below LV
compressing it but not compromising its function. Surgical exploration showed a
tumor at inferior part of LV
.
Pathology reported a benign fibromuscular tumor. Amiodarone was prescribed and
he was followed by serial echocardiography with no change in the size of the
tumor.
Syncopal episodes, however, continued and a sustained VT
was documented during one of the episodes. Interestingly VT originated from the
inferior part of LV. ECG showed a mildly prolonged QT interval and poor R
progression in right precordial leads
.
Frequent non-sustained runs and salvos
were detected by Holter monitoring.
A single chamber ICD was implanted at left subpectoral area
.
During over one year of follow-up he has had ICD pacing therapies for VT and one
inappropriate therapy for sinus tachycardia but no more syncope episodes.